J Turk Acad Dermatol 2013; 7 (1): 1371c1

Observation: Wooly hair is usually present at birth or infancy with a genetic linkage of autosomal dominant or recessive. Hair is curly, thick and often heavily pigmented. This condition has been reported with eye, teeth, cardiac anomalies. Also, keratosis pilaris atrophicans, ichtiyosis and deafness, palmoplantar keratoderma and Noonan syndrome may accompany wooly hair. We report two sisters with wooly hair, simultaneously developed an inflammatory tinea capitis (kerion). Our patients have neither a systemic disease nor eye, dental and other skin disorders. In their family; mother, two sisters, and one brother of them have also wooly hair without any other clinical associations. To our knowledge, this is the second, describes the association of wooly hair with tinea capitis. However, in the first report, mother and her son, also had keratosis follicularis spinulosa decalvans. As a result, presence of tinea capitis in both patients may be explained by the enhanced susceptibility to fungal infection in keratinizing disorders.